Supplementary Files
Keywords
Enfermería Pediátrica
Atención Primaria de Salud
Diagnóstico de Enfermería
Familia Glycogen Storage Disease Type II
Pediatric Nursing
Primary Health Care
Nursing Diagnosis
Family Doença de Depósito de Glicogênio Tipo II
Enfermagem Pediátrica
Atenção Primária à
Saúde
Diagnóstico de Enfermagem
Família
PlumX Metrics
Abstract
Aim: to identify diagnoses, interventions and expected nursing outcomes for the child with Pompe disease using the International Classification for Nursing Practice® 2017. Method: case study conducted in December 2017, with a mother of child with Pompe disease. Results: seventeen nursing diagnoses were presented, distributed among the demands of medicated, technological, habitual, modified, developmental, and family care. Discussion: the nursing diagnoses were related to the treatment and complications presented by the child as a result of Pompe disease, increased by the family needs to develop the care at home. Conclusion: it was verified that the classification of the nursing practices allowed creating more specialized possibilities to elaborate and execute a care plan based on the real needs of this child, allowing the possibility of generalization for the patients with the same disease.References
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