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Nursing care for children with Pompe disease: a case study

Eliana Roldão dos Santos Nonose, Ana Paula Keller de Matos, Rosane Meire Munhak da Silva, Ana Paula Contiero Toninato, Adriana Zilly, Regina Aparecida Garcia de Lima

Abstract


Aim: to identify diagnoses, interventions and expected nursing outcomes for the child with Pompe disease using the International Classification for Nursing Practice® 2017. Method: case study conducted in December 2017, with a mother of child with Pompe disease. Results: seventeen nursing diagnoses were presented, distributed among the demands of medicated, technological, habitual, modified, developmental, and family care. Discussion: the nursing diagnoses were related to the treatment and complications presented by the child as a result of Pompe disease, increased by the family needs to develop the care at home. Conclusion: it was verified that the classification of the nursing practices allowed creating more specialized possibilities to elaborate and execute a care plan based on the real needs of this child, allowing the possibility of generalization for the patients with the same disease.

Keywords


Glycogen Storage Disease Type II;Pediatric Nursing;Primary Health Care;Nursing Diagnosis;Family

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DOI: https://doi.org/10.17665/1676-4285.20186169



 

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